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Vascular hemostatic disease

MedGen UID:
154721
•Concept ID:
C0600502
•
Disease or Syndrome
Synonyms: Disorder, Vascular Hemostatic; Disorders, Vascular Hemostatic; Hemostatic Disorder; Hemostatic Disorder, Vascular; Hemostatic Disorders; Hemostatic Disorders, Vascular; Vascular Hemostatic Disorder; Vascular Hemostatic Disorders
SNOMED CT: Vascular hemostatic disease (21112004)
 
Monarch Initiative: MONDO:0003159

Definition

Pathological processes involving the integrity of blood circulation. Hemostasis depends on the integrity of blood vessels, blood fluidity, and blood coagulation. Majority of the hemostatic disorders are caused by disruption of the normal interaction between the vascular endothelium, the plasma proteins (including blood coagulation factors), and platelets. [from MONDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVVascular hemostatic disease

Professional guidelines

PubMed

Multiple myeloma: EHA-ESMO Clinical Practice Guidelines for diagnosis, treatment and follow-up(†).
Dimopoulos MA, Moreau P, Terpos E, Mateos MV, Zweegman S, Cook G, Delforge M, Hájek R, Schjesvold F, Cavo M, Goldschmidt H, Facon T, Einsele H, Boccadoro M, San-Miguel J, Sonneveld P, Mey U; EHA Guidelines Committee. Electronic address: guidelines@ehaweb.org; ESMO Guidelines Committee. Electronic address: clinicalguidelines@esmo.org
Ann Oncol 2021 Mar;32(3):309-322. Epub 2021 Feb 3 doi: 10.1016/j.annonc.2020.11.014. PMID: 33549387
European consensus-based recommendations for diagnosis and treatment of immunoglobulin A vasculitis-the SHARE initiative.
Ozen S, Marks SD, Brogan P, Groot N, de Graeff N, Avcin T, Bader-Meunier B, Dolezalova P, Feldman BM, Kone-Paut I, Lahdenne P, McCann L, Pilkington C, Ravelli A, van Royen A, Uziel Y, Vastert B, Wulffraat N, Kamphuis S, Beresford MW
Rheumatology (Oxford) 2019 Sep 1;58(9):1607-1616. doi: 10.1093/rheumatology/kez041. PMID: 30879080
International Myeloma Working Group updated criteria for the diagnosis of multiple myeloma.
Rajkumar SV, Dimopoulos MA, Palumbo A, Blade J, Merlini G, Mateos MV, Kumar S, Hillengass J, Kastritis E, Richardson P, Landgren O, Paiva B, Dispenzieri A, Weiss B, LeLeu X, Zweegman S, Lonial S, Rosinol L, Zamagni E, Jagannath S, Sezer O, Kristinsson SY, Caers J, Usmani SZ, Lahuerta JJ, Johnsen HE, Beksac M, Cavo M, Goldschmidt H, Terpos E, Kyle RA, Anderson KC, Durie BG, Miguel JF
Lancet Oncol 2014 Nov;15(12):e538-48. Epub 2014 Oct 26 doi: 10.1016/S1470-2045(14)70442-5. PMID: 25439696

Recent clinical studies

Etiology

A rational approach to functional high-risk myeloma.
Gay F, Bertuglia G, Mina R
Hematology Am Soc Hematol Educ Program 2023 Dec 8;2023(1):433-442. doi: 10.1182/hematology.2023000443. PMID: 38066896Free PMC Article
Non-secretory multiple myeloma: Diagnosis and management.
Charliński G, Jurczyszyn A
Adv Clin Exp Med 2022 Jan;31(1):95-100. doi: 10.17219/acem/141455. PMID: 34637200
Roadmap to cure multiple myeloma.
Rodriguez-Otero P, Paiva B, San-Miguel JF
Cancer Treat Rev 2021 Nov;100:102284. Epub 2021 Aug 31 doi: 10.1016/j.ctrv.2021.102284. PMID: 34597912
Fetal vascular malperfusion, an update.
Redline RW, Ravishankar S
APMIS 2018 Jul;126(7):561-569. doi: 10.1111/apm.12849. PMID: 30129125
Pathobiology and Diagnosis of Multiple Myeloma.
Brigle K, Rogers B
Semin Oncol Nurs 2017 Aug;33(3):225-236. Epub 2017 Jul 5 doi: 10.1016/j.soncn.2017.05.012. PMID: 28688533

Diagnosis

Scurvy.
Ishizuka K, Ohira Y
QJM 2022 Jul 9;115(7):475. doi: 10.1093/qjmed/hcac122. PMID: 35575388
Roadmap to cure multiple myeloma.
Rodriguez-Otero P, Paiva B, San-Miguel JF
Cancer Treat Rev 2021 Nov;100:102284. Epub 2021 Aug 31 doi: 10.1016/j.ctrv.2021.102284. PMID: 34597912
Updated Diagnostic Criteria and Staging System for Multiple Myeloma.
Rajkumar SV
Am Soc Clin Oncol Educ Book 2016;35:e418-23. doi: 10.1200/EDBK_159009. PMID: 27249749
Multiple myeloma.
Kyle RA, Rajkumar SV
Blood 2008 Mar 15;111(6):2962-72. doi: 10.1182/blood-2007-10-078022. PMID: 18332230Free PMC Article
Ehlers-Danlos syndrome--a historical review.
Parapia LA, Jackson C
Br J Haematol 2008 Apr;141(1):32-5. doi: 10.1111/j.1365-2141.2008.06994.x. PMID: 18324963

Therapy

Familial Cerebral Cavernous Malformations.
Zafar A, Quadri SA, Farooqui M, Ikram A, Robinson M, Hart BL, Mabray MC, Vigil C, Tang AT, Kahn ML, Yonas H, Lawton MT, Kim H, Morrison L
Stroke 2019 May;50(5):1294-1301. doi: 10.1161/STROKEAHA.118.022314. PMID: 30909834Free PMC Article
Bortezomib for the treatment of multiple myeloma.
Scott K, Hayden PJ, Will A, Wheatley K, Coyne I
Cochrane Database Syst Rev 2016 Apr 20;4(4):CD010816. doi: 10.1002/14651858.CD010816.pub2. PMID: 27096326Free PMC Article
Pomalidomide.
Lacy MQ, McCurdy AR
Blood 2013 Oct 3;122(14):2305-9. Epub 2013 Aug 23 doi: 10.1182/blood-2013-05-484782. PMID: 23974193
Consensus recommendations for the uniform reporting of clinical trials: report of the International Myeloma Workshop Consensus Panel 1.
Rajkumar SV, Harousseau JL, Durie B, Anderson KC, Dimopoulos M, Kyle R, Blade J, Richardson P, Orlowski R, Siegel D, Jagannath S, Facon T, Avet-Loiseau H, Lonial S, Palumbo A, Zonder J, Ludwig H, Vesole D, Sezer O, Munshi NC, San Miguel J; International Myeloma Workshop Consensus Panel 1
Blood 2011 May 5;117(18):4691-5. Epub 2011 Feb 3 doi: 10.1182/blood-2010-10-299487. PMID: 21292775Free PMC Article
Multiple myeloma.
Kyle RA, Rajkumar SV
Blood 2008 Mar 15;111(6):2962-72. doi: 10.1182/blood-2007-10-078022. PMID: 18332230Free PMC Article

Prognosis

Multiple myeloma: EHA-ESMO Clinical Practice Guidelines for diagnosis, treatment and follow-up(†).
Dimopoulos MA, Moreau P, Terpos E, Mateos MV, Zweegman S, Cook G, Delforge M, Hájek R, Schjesvold F, Cavo M, Goldschmidt H, Facon T, Einsele H, Boccadoro M, San-Miguel J, Sonneveld P, Mey U; EHA Guidelines Committee. Electronic address: guidelines@ehaweb.org; ESMO Guidelines Committee. Electronic address: clinicalguidelines@esmo.org
Ann Oncol 2021 Mar;32(3):309-322. Epub 2021 Feb 3 doi: 10.1016/j.annonc.2020.11.014. PMID: 33549387
A randomized phase 3 trial of zanubrutinib vs ibrutinib in symptomatic Waldenström macroglobulinemia: the ASPEN study.
Tam CS, Opat S, D'Sa S, Jurczak W, Lee HP, Cull G, Owen RG, Marlton P, Wahlin BE, Sanz RG, McCarthy H, Mulligan S, Tedeschi A, Castillo JJ, Czyz J, Fernández de Larrea C, Belada D, Libby E, Matous JV, Motta M, Siddiqi T, Tani M, Trneny M, Minnema MC, Buske C, Leblond V, Trotman J, Chan WY, Schneider J, Ro S, Cohen A, Huang J, Dimopoulos M
Blood 2020 Oct 29;136(18):2038-2050. doi: 10.1182/blood.2020006844. PMID: 32731259Free PMC Article
Once-weekly carfilzomib, pomalidomide, and low-dose dexamethasone for relapsed/refractory myeloma: a phase I/II study.
Bringhen S, Mina R, Cafro AM, Liberati AM, Spada S, Belotti A, Gaidano G, Patriarca F, Troia R, Fanin R, De Paoli L, Rossi G, Lombardo A, Bertazzoni P, Palumbo A, Sonneveld P, Boccadoro M
Leukemia 2018 Aug;32(8):1803-1807. Epub 2018 Jan 30 doi: 10.1038/s41375-018-0024-1. PMID: 29479061
Multiple myeloma and infections: a population-based study on 9253 multiple myeloma patients.
Blimark C, Holmberg E, Mellqvist UH, Landgren O, Björkholm M, Hultcrantz M, Kjellander C, Turesson I, Kristinsson SY
Haematologica 2015 Jan;100(1):107-13. Epub 2014 Oct 24 doi: 10.3324/haematol.2014.107714. PMID: 25344526Free PMC Article
Waldenström's macroglobulinemia.
Dimopoulos MA, Galani E, Matsouka C
Hematol Oncol Clin North Am 1999 Dec;13(6):1351-66. doi: 10.1016/s0889-8588(05)70130-1. PMID: 10626154

Clinical prediction guides

A rational approach to functional high-risk myeloma.
Gay F, Bertuglia G, Mina R
Hematology Am Soc Hematol Educ Program 2023 Dec 8;2023(1):433-442. doi: 10.1182/hematology.2023000443. PMID: 38066896Free PMC Article
Second Revision of the International Staging System (R2-ISS) for Overall Survival in Multiple Myeloma: A European Myeloma Network (EMN) Report Within the HARMONY Project.
D'Agostino M, Cairns DA, Lahuerta JJ, Wester R, Bertsch U, Waage A, Zamagni E, Mateos MV, Dall'Olio D, van de Donk NWCJ, Jackson G, Rocchi S, Salwender H, Bladé Creixenti J, van der Holt B, Castellani G, Bonello F, Capra A, Mai EK, Dürig J, Gay F, Zweegman S, Cavo M, Kaiser MF, Goldschmidt H, Hernández Rivas JM, Larocca A, Cook G, San-Miguel JF, Boccadoro M, Sonneveld P
J Clin Oncol 2022 Oct 10;40(29):3406-3418. Epub 2022 May 23 doi: 10.1200/JCO.21.02614. PMID: 35605179
The Beighton Score as a measure of generalised joint hypermobility.
Malek S, Reinhold EJ, Pearce GS
Rheumatol Int 2021 Oct;41(10):1707-1716. Epub 2021 Mar 18 doi: 10.1007/s00296-021-04832-4. PMID: 33738549Free PMC Article
Platelet function tests: a comparative review.
Paniccia R, Priora R, Liotta AA, Abbate R
Vasc Health Risk Manag 2015;11:133-48. Epub 2015 Feb 18 doi: 10.2147/VHRM.S44469. PMID: 25733843Free PMC Article
Review of 1027 patients with newly diagnosed multiple myeloma.
Kyle RA, Gertz MA, Witzig TE, Lust JA, Lacy MQ, Dispenzieri A, Fonseca R, Rajkumar SV, Offord JR, Larson DR, Plevak ME, Therneau TM, Greipp PR
Mayo Clin Proc 2003 Jan;78(1):21-33. doi: 10.4065/78.1.21. PMID: 12528874

Recent systematic reviews

Relapsed and refractory multiple myeloma: A systematic review and network meta-analysis of the efficacy of novel therapies.
Minakata D, Fujiwara SI, Yokoyama D, Noguchi A, Aoe S, Oyama T, Koyama S, Murahashi R, Nakashima H, Hyodo K, Ikeda T, Kawaguchi SI, Toda Y, Ito S, Nagayama T, Mashima K, Umino K, Morita K, Ashizawa M, Yamamoto C, Hatano K, Sato K, Ohmine K, Kanda Y
Br J Haematol 2023 Mar;200(6):694-703. Epub 2023 Jan 20 doi: 10.1111/bjh.18654. PMID: 36661264
Management of mixed cryoglobulinemia with rituximab: evidence and consensus-based recommendations from the Italian Study Group of Cryoglobulinemia (GISC).
Quartuccio L, Bortoluzzi A, Scirè CA, Marangoni A, Del Frate G, Treppo E, Castelnovo L, Saccardo F, Zani R, Candela M, Fraticelli P, Mazzaro C, Renoldi P, Scaini P, Filippini DA, Visentini M, Scarpato S, Giuggioli D, Mascia MT, Sebastiani M, Zignego AL, Lauletta G, Fiorilli M, Casato M, Ferri C, Pietrogrande M, Pioltelli PE, De Vita S, Monti G, Galli M
Clin Rheumatol 2023 Feb;42(2):359-370. Epub 2022 Sep 28 doi: 10.1007/s10067-022-06391-w. PMID: 36169798Free PMC Article
A Comprehensive Review of Hepatic Hemangioma Management.
Aziz H, Brown ZJ, Baghdadi A, Kamel IR, Pawlik TM
J Gastrointest Surg 2022 Sep;26(9):1998-2007. Epub 2022 Jun 15 doi: 10.1007/s11605-022-05382-1. PMID: 35705835
Extramedullary disease in multiple myeloma: a systematic literature review.
Bladé J, Beksac M, Caers J, Jurczyszyn A, von Lilienfeld-Toal M, Moreau P, Rasche L, Rosiñol L, Usmani SZ, Zamagni E, Richardson P
Blood Cancer J 2022 Mar 21;12(3):45. doi: 10.1038/s41408-022-00643-3. PMID: 35314675Free PMC Article
Physical therapy treatment of hypermobile Ehlers-Danlos syndrome: A systematic review.
Reychler G, De Backer MM, Piraux E, Poncin W, Caty G
Am J Med Genet A 2021 Oct;185(10):2986-2994. Epub 2021 Jun 19 doi: 10.1002/ajmg.a.62393. PMID: 34145717

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