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Hereditary cardiac anomaly

MedGen UID:
1842341
Concept ID:
C5680759
Congenital Abnormality
Synonym: Genetic cardiac anomaly
 
Orphanet: ORPHA271853

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVHereditary cardiac anomaly

Professional guidelines

PubMed

Adams D, Ando Y, Beirão JM, Coelho T, Gertz MA, Gillmore JD, Hawkins PN, Lousada I, Suhr OB, Merlini G
J Neurol 2021 Jun;268(6):2109-2122. Epub 2020 Jan 6 doi: 10.1007/s00415-019-09688-0. PMID: 31907599Free PMC Article
Drezner JA, Sharma S, Baggish A, Papadakis M, Wilson MG, Prutkin JM, Gerche A, Ackerman MJ, Borjesson M, Salerno JC, Asif IM, Owens DS, Chung EH, Emery MS, Froelicher VF, Heidbuchel H, Adamuz C, Asplund CA, Cohen G, Harmon KG, Marek JC, Molossi S, Niebauer J, Pelto HF, Perez MV, Riding NR, Saarel T, Schmied CM, Shipon DM, Stein R, Vetter VL, Pelliccia A, Corrado D
Br J Sports Med 2017 May;51(9):704-731. Epub 2017 Mar 3 doi: 10.1136/bjsports-2016-097331. PMID: 28258178
Shovlin CL, Letarte M
Thorax 1999 Aug;54(8):714-29. doi: 10.1136/thx.54.8.714. PMID: 10413726Free PMC Article

Recent clinical studies

Etiology

Drezner JA, Sharma S, Baggish A, Papadakis M, Wilson MG, Prutkin JM, Gerche A, Ackerman MJ, Borjesson M, Salerno JC, Asif IM, Owens DS, Chung EH, Emery MS, Froelicher VF, Heidbuchel H, Adamuz C, Asplund CA, Cohen G, Harmon KG, Marek JC, Molossi S, Niebauer J, Pelto HF, Perez MV, Riding NR, Saarel T, Schmied CM, Shipon DM, Stein R, Vetter VL, Pelliccia A, Corrado D
Br J Sports Med 2017 May;51(9):704-731. Epub 2017 Mar 3 doi: 10.1136/bjsports-2016-097331. PMID: 28258178
Sharma S, Drezner JA, Baggish A, Papadakis M, Wilson MG, Prutkin JM, La Gerche A, Ackerman MJ, Borjesson M, Salerno JC, Asif IM, Owens DS, Chung EH, Emery MS, Froelicher VF, Heidbuchel H, Adamuz C, Asplund CA, Cohen G, Harmon KG, Marek JC, Molossi S, Niebauer J, Pelto HF, Perez MV, Riding NR, Saarel T, Schmied CM, Shipon DM, Stein R, Vetter VL, Pelliccia A, Corrado D
J Am Coll Cardiol 2017 Feb 28;69(8):1057-1075. doi: 10.1016/j.jacc.2017.01.015. PMID: 28231933
Cummings KW, Bhalla S
Clin Chest Med 2015 Jun;36(2):235-48, viii. Epub 2015 Mar 26 doi: 10.1016/j.ccm.2015.02.007. PMID: 26024602
Meuwissen ME, Halley DJ, Smit LS, Lequin MH, Cobben JM, de Coo R, van Harssel J, Sallevelt S, Woldringh G, van der Knaap MS, de Vries LS, Mancini GM
Genet Med 2015 Nov;17(11):843-53. Epub 2015 Feb 26 doi: 10.1038/gim.2014.210. PMID: 25719457
Galanello R, Origa R
Orphanet J Rare Dis 2010 May 21;5:11. doi: 10.1186/1750-1172-5-11. PMID: 20492708Free PMC Article

Diagnosis

Obi CA, Mostertz WC, Griffin JM, Judge DP
Methodist Debakey Cardiovasc J 2022;18(2):17-26. Epub 2022 Mar 14 doi: 10.14797/mdcvj.1066. PMID: 35414855Free PMC Article
Adams D, Ando Y, Beirão JM, Coelho T, Gertz MA, Gillmore JD, Hawkins PN, Lousada I, Suhr OB, Merlini G
J Neurol 2021 Jun;268(6):2109-2122. Epub 2020 Jan 6 doi: 10.1007/s00415-019-09688-0. PMID: 31907599Free PMC Article
Drezner JA, Sharma S, Baggish A, Papadakis M, Wilson MG, Prutkin JM, Gerche A, Ackerman MJ, Borjesson M, Salerno JC, Asif IM, Owens DS, Chung EH, Emery MS, Froelicher VF, Heidbuchel H, Adamuz C, Asplund CA, Cohen G, Harmon KG, Marek JC, Molossi S, Niebauer J, Pelto HF, Perez MV, Riding NR, Saarel T, Schmied CM, Shipon DM, Stein R, Vetter VL, Pelliccia A, Corrado D
Br J Sports Med 2017 May;51(9):704-731. Epub 2017 Mar 3 doi: 10.1136/bjsports-2016-097331. PMID: 28258178
Sharma S, Drezner JA, Baggish A, Papadakis M, Wilson MG, Prutkin JM, La Gerche A, Ackerman MJ, Borjesson M, Salerno JC, Asif IM, Owens DS, Chung EH, Emery MS, Froelicher VF, Heidbuchel H, Adamuz C, Asplund CA, Cohen G, Harmon KG, Marek JC, Molossi S, Niebauer J, Pelto HF, Perez MV, Riding NR, Saarel T, Schmied CM, Shipon DM, Stein R, Vetter VL, Pelliccia A, Corrado D
J Am Coll Cardiol 2017 Feb 28;69(8):1057-1075. doi: 10.1016/j.jacc.2017.01.015. PMID: 28231933
Galanello R, Origa R
Orphanet J Rare Dis 2010 May 21;5:11. doi: 10.1186/1750-1172-5-11. PMID: 20492708Free PMC Article

Therapy

Liu S, Zhang Q, Liu W, Zheng L, Zhou J, Huang X
J Int Med Res 2022 Mar;50(3):3000605221085427. doi: 10.1177/03000605221085427. PMID: 35380076Free PMC Article
Baldacci S, Gorini F, Santoro M, Pierini A, Minichilli F, Bianchi F
Epidemiol Prev 2018 May-Aug;42(3-4 Suppl 1):1-34. doi: 10.19191/EP18.3-4.S1.P001.057. PMID: 30066535
Xu MN, Zhang M, Xu Y, Wang M, Yuan SM
J Craniofac Surg 2018 Oct;29(7):1876-1879. doi: 10.1097/SCS.0000000000004745. PMID: 30052610
Samuel BP, Duffner UA, Abdel-Mageed AS, Vettukattil JJ
Pediatr Dermatol 2015 Jul-Aug;32(4):e165-6. Epub 2015 Apr 9 doi: 10.1111/pde.12589. PMID: 25854548
O'Brien MD, Gilmour-White S
BMJ 1993 Aug 21;307(6902):492-5. doi: 10.1136/bmj.307.6902.492. PMID: 8400940Free PMC Article

Prognosis

Obi CA, Mostertz WC, Griffin JM, Judge DP
Methodist Debakey Cardiovasc J 2022;18(2):17-26. Epub 2022 Mar 14 doi: 10.14797/mdcvj.1066. PMID: 35414855Free PMC Article
Osovska N, Kuzminova N, Ovcharuk M, Serhiychuk O
Georgian Med News 2016 Jun;(255):66-77. PMID: 27441539
Meuwissen ME, Halley DJ, Smit LS, Lequin MH, Cobben JM, de Coo R, van Harssel J, Sallevelt S, Woldringh G, van der Knaap MS, de Vries LS, Mancini GM
Genet Med 2015 Nov;17(11):843-53. Epub 2015 Feb 26 doi: 10.1038/gim.2014.210. PMID: 25719457
Massoure PL, Latremouille C, Lamblin G, Leca F
Cardiovasc J Afr 2012 Jul 12;23(6):e19-20. doi: 10.5830/CVJA-2012-011. PMID: 22832481
Galanello R, Origa R
Orphanet J Rare Dis 2010 May 21;5:11. doi: 10.1186/1750-1172-5-11. PMID: 20492708Free PMC Article

Clinical prediction guides

da Palma MM, Igelman AD, Ku C, Burr A, You JY, Place EM, Wang NK, Oh JK, Branham KE, Zhang X, Ahn J, Gorin MB, Lam BL, Ronquillo CC, Bernstein PS, Nagiel A, Huckfeldt R, Cabrera MT, Kelly JP, Bakall B, Iannaccone A, Hufnagel RB, Zein WM, Koenekoop RK, Birch DG, Yang P, Fahim AT, Pennesi ME
Invest Ophthalmol Vis Sci 2021 Jun 1;62(7):27. doi: 10.1167/iovs.62.7.27. PMID: 34185059Free PMC Article
Meuwissen ME, Halley DJ, Smit LS, Lequin MH, Cobben JM, de Coo R, van Harssel J, Sallevelt S, Woldringh G, van der Knaap MS, de Vries LS, Mancini GM
Genet Med 2015 Nov;17(11):843-53. Epub 2015 Feb 26 doi: 10.1038/gim.2014.210. PMID: 25719457
Uzak AS, Fryns JP, Dundar M
Genet Couns 2014;25(2):159-69. PMID: 25059014
Lhuaire M, Jestin A, Boulagnon C, Loock M, Doco-Fenzy M, Gaillard D, Diebold MD, Avisse C, Labrousse M
Birth Defects Res A Clin Mol Teratol 2013 Mar;97(3):123-32. doi: 10.1002/bdra.23125. PMID: 23526679
Massoure PL, Latremouille C, Lamblin G, Leca F
Cardiovasc J Afr 2012 Jul 12;23(6):e19-20. doi: 10.5830/CVJA-2012-011. PMID: 22832481

Recent systematic reviews

He X, Tian Z, Guan H, Zhang S
Orphanet J Rare Dis 2022 Sep 2;17(1):337. doi: 10.1186/s13023-022-02481-9. PMID: 36056432Free PMC Article
Bruno M, Castaño A, Burton A, Grodin JL
Heart Fail Rev 2021 Jan;26(1):35-45. doi: 10.1007/s10741-020-10010-8. PMID: 32794090Free PMC Article
Wijngaarde CA, Blank AC, Stam M, Wadman RI, van den Berg LH, van der Pol WL
Orphanet J Rare Dis 2017 Apr 11;12(1):67. doi: 10.1186/s13023-017-0613-5. PMID: 28399889Free PMC Article

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