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Extracavitary Primary Effusion Lymphoma

MedGen UID:
1666925
Concept ID:
C4725707
Neoplastic Process
Synonym: Extracavitary PEL

Definition

A rare HHV8-positive B-cell lymphoma indistinguishable from primary effusion lymphoma presenting as solid tumor mass. (WHO 2017) [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVExtracavitary Primary Effusion Lymphoma

Professional guidelines

PubMed

Ramirez-Gamero A, Martínez-Cordero H, Beltrán BE, Florindez J, Malpica L, Castillo JJ
Am J Hematol 2024 Aug;99(8):1586-1594. Epub 2024 May 20 doi: 10.1002/ajh.27376. PMID: 38767403

Recent clinical studies

Etiology

Ramirez-Gamero A, Martínez-Cordero H, Beltrán BE, Florindez J, Malpica L, Castillo JJ
Am J Hematol 2024 Aug;99(8):1586-1594. Epub 2024 May 20 doi: 10.1002/ajh.27376. PMID: 38767403
Ibrahim U, Saqib A, Mohammad F, Ding J, Hussein S, Atallah JP
Postgrad Med 2017 Apr;129(3):402-407. Epub 2017 Feb 13 doi: 10.1080/00325481.2017.1286925. PMID: 28122468
Guillet S, Gérard L, Meignin V, Agbalika F, Cuccini W, Denis B, Katlama C, Galicier L, Oksenhendler E
Am J Hematol 2016 Feb;91(2):233-7. doi: 10.1002/ajh.24251. PMID: 26799611
Medeiros BC, Maness LJ, Bauer FA, Ross JW, Kapur D
Conn Med 2000 Oct;64(10):591-4. PMID: 11100630

Diagnosis

Ramirez-Gamero A, Martínez-Cordero H, Beltrán BE, Florindez J, Malpica L, Castillo JJ
Am J Hematol 2024 Aug;99(8):1586-1594. Epub 2024 May 20 doi: 10.1002/ajh.27376. PMID: 38767403
Krishnamurthy K, Sriganeshan V
Blood 2020 Apr 2;135(14):1190. doi: 10.1182/blood.2019004506. PMID: 32243520
Shah NN, Harrison N, Stonecypher M, Frank D, Amorosa V, Svoboda J
Clin Lymphoma Myeloma Leuk 2014 Oct;14(5):e157-60. Epub 2014 Jun 11 doi: 10.1016/j.clml.2014.05.001. PMID: 25027567
Arora M, Cossor FI
Blood 2012 Mar 22;119(12):2707. doi: 10.1182/blood-2011-04-319103. PMID: 22548219
El-Ayass W, Yu EM, Karcher DS, Aragon-Ching JB
Clin Lymphoma Myeloma Leuk 2012 Apr;12(2):144-7. Epub 2012 Jan 20 doi: 10.1016/j.clml.2011.12.003. PMID: 22264773

Therapy

Ramirez-Gamero A, Martínez-Cordero H, Beltrán BE, Florindez J, Malpica L, Castillo JJ
Am J Hematol 2024 Aug;99(8):1586-1594. Epub 2024 May 20 doi: 10.1002/ajh.27376. PMID: 38767403
Zanelli M, Bertuzzi C, Zizzo M, Martino G, Sabattini E, Ascani S
Br J Haematol 2019 Dec;187(5):555. Epub 2019 Sep 13 doi: 10.1111/bjh.16196. PMID: 31515799
Guillet S, Gérard L, Meignin V, Agbalika F, Cuccini W, Denis B, Katlama C, Galicier L, Oksenhendler E
Am J Hematol 2016 Feb;91(2):233-7. doi: 10.1002/ajh.24251. PMID: 26799611
Shah NN, Harrison N, Stonecypher M, Frank D, Amorosa V, Svoboda J
Clin Lymphoma Myeloma Leuk 2014 Oct;14(5):e157-60. Epub 2014 Jun 11 doi: 10.1016/j.clml.2014.05.001. PMID: 25027567
El-Ayass W, Yu EM, Karcher DS, Aragon-Ching JB
Clin Lymphoma Myeloma Leuk 2012 Apr;12(2):144-7. Epub 2012 Jan 20 doi: 10.1016/j.clml.2011.12.003. PMID: 22264773

Prognosis

Ramirez-Gamero A, Martínez-Cordero H, Beltrán BE, Florindez J, Malpica L, Castillo JJ
Am J Hematol 2024 Aug;99(8):1586-1594. Epub 2024 May 20 doi: 10.1002/ajh.27376. PMID: 38767403
Di Napoli A, Soma L, Quintanilla-Martinez L, de Leval L, Leoncini L, Zamò A, Ng SB, Ondrejka SL, Climent F, Wotherspoon A, Dirnhofer S
Virchows Arch 2023 Sep;483(3):299-316. Epub 2023 Aug 9 doi: 10.1007/s00428-023-03599-2. PMID: 37555981Free PMC Article
Campogiani L, Cerva C, Maffongelli G, Teti E, Pupo L, Vaccarini S, Cantonetti M, Pennica A, Andreoni M, Sarmati L
AIDS Res Ther 2019 Jul 27;16(1):15. doi: 10.1186/s12981-019-0230-6. PMID: 31351487Free PMC Article
Guillet S, Gérard L, Meignin V, Agbalika F, Cuccini W, Denis B, Katlama C, Galicier L, Oksenhendler E
Am J Hematol 2016 Feb;91(2):233-7. doi: 10.1002/ajh.24251. PMID: 26799611
Pielasinski U, Santonja C, Rodríguez-Pinilla SM, Requena L
J Cutan Pathol 2014 Sep;41(9):745-53. Epub 2014 Jul 28 doi: 10.1111/cup.12368. PMID: 24917369

Clinical prediction guides

Ramirez-Gamero A, Martínez-Cordero H, Beltrán BE, Florindez J, Malpica L, Castillo JJ
Am J Hematol 2024 Aug;99(8):1586-1594. Epub 2024 May 20 doi: 10.1002/ajh.27376. PMID: 38767403
Guillet S, Gérard L, Meignin V, Agbalika F, Cuccini W, Denis B, Katlama C, Galicier L, Oksenhendler E
Am J Hematol 2016 Feb;91(2):233-7. doi: 10.1002/ajh.24251. PMID: 26799611

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